Haploinsufficiency of KMT2D is sufficient to cause Kabuki syndrome and is compatible with life.

Mol Genet Genomic Med
Authors
Abstract

We present the first patient described with haploinsufficency of KMT2D leading to Kabuki syndrome. Deletion of KMT2D has been thought to be lethal, but here we describe a patient with KMT2D deletion and classical Kabuki syndrome phenotype.

Year of Publication
2020
Journal
Mol Genet Genomic Med
Volume
8
Issue
2
Pages
e1072
Date Published
2020 Feb
ISSN
2324-9269
DOI
10.1002/mgg3.1072
PubMed ID
31814321
PubMed Central ID
PMC7005614
Links
Grant list
WT_ / Wellcome Trust / United Kingdom
Louma G Foundation
195835-051 / Icelandic Research Fund